Title: A window that is lost in time which is defying the odds – “A Rare Case of Pulmonary Artery Hypertension”
Authors: Ezhilkumaar Murthyraajan, M.K. Uthayasankar, D.V. Rangarajan
DOI: https://dx.doi.org/10.18535/jmscr/v13i03.04
Abstract
Aortopulmonary window is an uncommon congenital heart disease that can increase pulmonary vascular resistance and result in heart failure and recurrent respiratory infections. The condition is often fatal in childhood. Here, we present a case of a 35-year-old male with a large aortopulmonary window, complicated by Eisenmenger syndrome, who has survived without surgical intervention for past 35 years.
Keywords: Congenital heart disease, Pulmonary vascular resistance, Aortopulmonary window, Eisenmenger syndrome, Heart failure, Differential ABG, Right heart catheterization, Vasoreactivity, Endothelin receptor antagonist, Phosphodiesterase 5 inhibitor, Tunnel flap, Pan-digital clubbing, Central cyanosis, Biventricular hypertrophy.
