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Category: Volume 12 Issue 04 April 2024
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Title: Infantile Fibrosarcoma Presenting as Neck Mass: A Case Report

Author: Dr Yasap Tana

 DOI: https://dx.doi.org/10.18535/jmscr/v12i04.03

Abstract

A one year old boy presented with a mass in the posterior triangle of left side of neck for ten months with rapid increase in size since one month. Radio-imaging was done. He underwent surgery, the mass was excised and the histopathological examination was done. Clinically, it was thought to be as schwannoma.

Tumor measured 10 x 8 x 6 cm approximately, fixed with underlying tissue, venous prominence seen on bosselated surface and was non-tender.

Microscopically, showed a cellular neoplasm composed of spindle cells arranged in herringbone pattern, also as fascicles and bundles, with focal area showing slit like thin-walled vessels simulating hemangiopericytoma like vasculature. Focally, shows infiltration of muscle and fat. Immunohistochemistry study was performed.

Correlating histology with clinical, radiology and immunohistochemistry findings, the patient was diagnosed as a case of Infantile Fibrosarcoma of neck region, a relatively rare malignant fibroblastic tumor, occurring mostly in infancy, often misdiagnosed with benign tumor.

Keywords: Cellular, herringbone pattern, hemangiopericytoma, immunohistochemistry, fibroblastic.

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Corresponding Author

Dr Yasap Tana

Consultant Pathologist, Department of Pathology, Tomo Riba Institute of Health and Medical Sciences, Naharlagun, Arunachal Pradesh, India

(Former Senior Resident, Department of Pathology, Government Medical College, Thrissur, Kerala, India)