Epithelioid sarcoma is a rare variety of malignant soft tissue sarcoma of uncertain differentiation that affects young adults mostly involves upper arm especially arm and wrist. It has a high rate of recurrence and metastasis. A 55-year-old male presented in December 2011 with a swelling over right scapular region (near angle of scapula). The patient gave a history of swelling from 6 months. Local excision was done 2 times from 2014 to 2016. Each time the recurrence was just distal to previous one. For the third recurrence just adjacent to it wide local excision was done. Immunohistochemistry (IHC) showed expression of Vimentin, Pan-CK: Focal positive, EMA: Focal positive, LCA: negative, CD-99: Negative,. IHC confirmed the diagnosis of epithelioid sarcoma of axillary region. Patient received adjuvant chemotherapy followed by local radiotherapy. Patient remained asymptomatic for 2 years when follow up PET-CT was suggestive of lung metastasis. Thus, doxorubicin based chemotherapy has been planned.

Keywords: Doxorubicin, epithelioid sarcoma, immunohistochemistry, wide local excision, Scapula.

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Raza MW