Title: Acute Flaccid Quadriplegia: A Rare Case of Adult Onset Bartter’s Syndrome
Authors: Dr Ankur Banik, Dr Sourish Chatterjee, Dr Uttam Biswas
DOI: https://dx.doi.org/10.18535/jmscr/v5i6.91
Abstract
Bartter’s syndrome is a rare autosomal recessive disorder which generally presents in paediatric age group. It is characterised by hypokalemia, hypocalcemia, hypercalciuria, metabolic alkalosis, hyper-reninemic hyperaldosteronism and a normal blood pressure. We report a case of adult onset Bartter’s syndrome, in a 41 year old man who presented with acute onset quadriplegia along with weakness of neck muscles. We report this case because adult onset Bartter’s syndrome is very rare and with the best of our knowledge, so far, very few case reports are available from India in which the presentation was with quadriplegia and neck weakness.
Keywords: Bartter’s syndrome, hypokalemia, acute flaccid paralysis.
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