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Category: Volume 10 Issue 11 November 2022
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Title: Cutaneous Mucinous Cystadenocarcinoma

Authors: Dr MD Aqueel, Dr Aditya Uttam

 DOI: https://dx.doi.org/10.18535/jmscr/v10i11.20

Abstract

Introduction

Primary cutaneous mucinous carcinoma (PCMC) is a rare low-grade malignant neoplasm originally believed to be of eccrine origin(1) These tumors are slow growing, arising on the face (particularly the eyelids), axilla, scalp, and trunk of middle-aged and older individuals(2). The lesions typically present as erythematous, asymptomatic nodules measuring 0.5 to 7 cm in diameter; however, larger variants have been reported(3-5) The contemporary, but still somewhat controversial, view is that these tumors actually demonstrate apocrine-type differentiation(6-8)

Morbidity related to PCMC is primarily associated with incomplete resection(9,10) While PCMC tends to grow slowly and have a good prognosis, late recurrences and rare metastases have been reported. Recurrence portends substantial morbidity, as recurrent tumors do not tend to respond to radiation treatment or chemotherapy(11)

As is the case with many rare nonmelanoma tumors, there is no standard of care for the surgical treatment of PCMC. Currently employed modes of treatment for PCMC vary from standard excision to wide local excision, including dissection of regional lymph nodes(11). Mohs surgery was first introduced as a means for PCMC treatment by Weber et al(11,12) in 1988. Due to the rarity of PCMS, the studies included were observational, primarily case reports and case series

Case Report

A 64 year old male presented to our clinics with chief complains of left axillary swelling for 4 month which was histologically proven to be cutaneous deposits of mucinous cystadenocarcinoma

Patient was examined and found to have no abnormality in oral cavity and no palpable cervical  and supraclavicular lymph nodes. In right axilla approximately 3cm*2.5cm firm non tender mobile lymph node was palpable.L axilla was NAD.

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Corresponding Author

Dr MD Aqueel

SR SNMC Agra