Title: Pregnancy Associated Atypical Hemolytic Uremic Syndrome: A Rare Case Report
Authors: Dr Manvi Katoch, Dr Tanvi Katoch
DOI: https://dx.doi.org/10.18535/jmscr/v9i5.35
Abstract
Atypical hemolytic uremic syndrome has a genetic predisposition. Pregnancy is a trigger to develop the disease and is a rare entity. It leads to hemolysis in microvasculature, acute renal failure, and thrombocytopenia. The disease is associated with a poor prognosis and needs early treatment initiation. 34-year-old P4L2 with post-partum hemorrhage was managed at our centre following which she had acute kidney injury, thrombocytopenia, and repeated fall in hemoglobin. A diagnosis of P-aHUS was made after ruling out other differentials and she was managed with hemodialysis and plasma exchange.
Keywords: pregnancy, atypical hemolytic uremic syndrome, eculizumab, plasma exchange.
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