Title: Wilsons Disease – A Varied Histological Spectrum
Authors: Dr Milap Shan, Dr M. Srividya, Dr Sindhu Kotla, Dr G. Archana
DOI: https://dx.doi.org/10.18535/jmscr/v8i9.50
Abstract
Wilsons disease is an autosomal recessive disorder of copper metabolism that mostly presents with hepatic dysfunction followed by neurologic/psychiatric symptoms and hematological problems. Though the defect is already present at birth it rarely manifests before 5 years of age. Here we are presenting four cases of wilsons disease presenting with variable histopathological presentations at our hospital during the year 2020.
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