Title: Surgical Management of Complex Hypertrophic Cardiomyopathy Causing Severe Mitral Regurgitation in a Child
Authors: Dr Ajit Kumar Padhy, Dr Sistla Vpl Chandrakumar, Dr Kunwar Sidharth Sourabh, Dr Sankalp Rahi, Dr Ira Balakrishnan, Dr Anubhav Gupta
DOI: https://dx.doi.org/10.18535/jmscr/v8i3.46
Abstract
Mitral leaflet elongation and subvalvular apparatus deformation can be seen in obstructive septal hypertrophy. In such hypertrophic cardiomyopathy (HCM) mitral malformations, the Mitral valve repair will not suffice to reverse the pathology unless surgical myomectomy is done. Outcome is more gratifying when left ventricular outflow tract obstruction (LVOTO) is eliminated along with abolition of systolic anterior motion (SAM) of mitral leaflet. Trans-esophageal echocardiography (TEE) play a major role in making surgical decision on operating table.
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