Title: A Giant Chondrosarcoma Born on Primary Osteochondroma – A Rare Case Report

Authors: Dr Vinay Kumar.J.Rajendra, Dr Sruthy Harshan

 DOI: https://dx.doi.org/10.18535/jmscr/v8i3.38

Abstract

   

Background: Chondrosarcoma is a rare malignant tumor of the bone. Secondary chondrosarcoma originating from a primary osteochondroma is extremely rare and the data show that the reported incidence of shoulder osteochondroma is very low. We report the case of a 28 yr old male patient with Chondrosarcoma secondary to malignant transformation of an Osteochondroma of left shoulder. The patient was diagnosed with left shoulder Osteochondroma 7 years back for which tumour excision was done. He currently presented with a 20 x 20 x 15 cm swelling over the left scapular region since two years. MRI of Shoulder revealed a large expansile altered signal intensity lesion arising from the left scapula. Biopsy showed roughly cartilaginous appearance and was diagnosed to be well differentiated Chondrosarcoma. Patient was therefore a candidate for a large resection. HRCT thorax was done which showed no parenchymal lung lesion. Intra-operatively, Glenoid capsule, superior and lateral cord of Brachial plexus was involved. Histopathology showed secondary low grade Chondrosarcoma of scapula with all resected margins free of tumour. He is now at 1 year of surgical resection, and is doing well with restriction in movements at shoulder joint . 

Keywords: Chondrosarcoma , osteochondroma , scapula

References

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Corresponding Author

Dr Vinay Kumar J Rajendra

Associate Professor and Consultant Surgical Oncologist, Department of Surgical Oncology, K.S. Hegde Medical Academy, Deralakatte, Mangalore