Title: A Study of Unusual Renal Neoplasms of Childhood in a Tertiary Care Centre of Eastern India for last 5 years
Author: Dr Sanghamitra Mukherjee
DOI: https://dx.doi.org/10.18535/jmscr/v7i12.96
Abstract
Paediatric renal neoplasms present special challenges to the surgical pathologists because of their histological diversity. Wilms, tumor is the commonest amongst these. Lack of familiarity with the other pediatric renal neoplasms can lead to erroneous diagnosis. All resected specimens of kidney tumors over a period of 5 years were studied. Out of total 36 cases, there were 27 cases of Wilms, tumor. Amongst the other 9 cases, there were 3 cases of congenital mesoblastic nephroma, 2 cases of multicystic nephroma, 3 cases of clear cell sarcoma and 1 case of rhabdoid tumor. The cases of mesoblastic nephroma and multicystic nephroma are all doing well on follow up but the cases of clear cell sarcoma and rhabdoid tumor were associated with poor prognosis.
Keywords: Mesoblastic Nephroma, Multicystic Nephroma, Clear Cell Sarcoma, Rhabdoid tumor.
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