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Category: Volume 07 Issue 11 November 2019
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Title: Optic Nerve Aplasia (Uniateral)

Authors: Dr Kamla Prasad, Dr. Rahmat Ali

 DOI: https://dx.doi.org/10.18535/jmscr/v7i11.106

Abstract

Optic nerve aplasia is a rare developmental anomaly consisting of absence of the optic nerve, retinal blood vessels and ganglion cells. ONA may be an isolated finding or associated with congenital ocular and non-ocular abnormalities. It has frequent association with microphthalmos and other malformations confined to the involved eye. Unilateral ONA is generally associated with normal brain development, while bilateral ONA is usually accompanied by other central nervous system (CNS) abnormalities.

Keywords: Microcornea, Enophthalmos, Magnetic resonance imaging (MRI), Optic disc, ONA, VEP.

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Corresponding Author

Dr Rahmat Ali

Associate Professor & H.O.D Ortho., Maharshi Vashishth, Autonomous Govt. Medical College, Basti (U.P.)