Title: Hirayama Disease
Authors: Dr Meghana Murthy, Dr Ravi B.N, Dr H. Vasudeva Naik
DOI: https://dx.doi.org/10.18535/jmscr/v6i8.33
Abstract
Hirayama diseaseis a relatively rare myelopathy, a self limiting juvenile spinal muscular atrophy of the distal upper limbs. The exact etiology is unknown however a limited form of ischemic cervical myelopathy has been proposed as the cause. It affects mostly males in second to third decade. Cervical MRI is the preferred investigation. We report a case of Hirayama disease in a 24 year Indian male presenting with gradually progressive weakness and wasting of both the hands.
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