Title: Anaesthetic Management of Scoliotic Deformity with Wilson’s Disease
Authors: Vasudha Gupta, Ajeet Kumar, Bhavana Kayarat
DOI: https://dx.doi.org/10.18535/jmscr/v6i4.180
Abstract
Wilson’s disease is an inherited autosomal recessive disorder of copper metabolism. As a consequence copper accumulates in liver, brain, kidney and red blood cells. Patients may develop chronic liver disease, hemolytic anaemia and neurological symptoms. Hepatic involvement may interfere with metabolism of various anaesthetic drugs. Anaesthesia for deformity correction of scoliosis itself is challenging and associated with various complications. Very few cases has been reported of anaesthetic management in patients with wilson’s disease associated with scoliosis.
Keywords: Wilson’s disease, scoliosis, General Anaesthesia.
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